Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature

Pradosh Kumar Sarangi; H. S. Sagar; Sanjay Kumar Nahak; Jayashree Mohanty; Sasmita Parida

doi:10.5455/jmas.252500

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Case Report
Online Published: 29 Jan 2017

J Med Allied Sci. 2017; 7(1): 67-71

doi: 10.5455/jmas.252500

Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida.

Abstract
Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood accounting for 0.25-0.5% of primary lung tumors. PPB is a dysontogenic tumor composed of immature malignant epithelial and/or mesenchymal tissues whose features may resemble early embryological lung tissues. It is the pulmonary analog of other tumors of childhood including Wilms' tumor, neuroblastoma, hepatoblastoma, pancreatoblastoma and retinoblastoma. Morphologically, PPB has three types (I, II, and III). A fourth type (Ir) was added in 2006 by PPB registry. Type II and III are very aggressive malignancies with metastatic potential. Bilateral PPB is very rare. To the best of our knowledge, only two cases of bilateral PPB have been reported. No cases of bilateral PPB have been reported from India. Herein, we are reporting a case of bilateral PPB (type II) in a 2-year-old girl who presented with cough, dyspnea and mild fever for past 4 months. She died few days after admission.

Key words: Bilateral pleuropulmonary blastoma, Bronchogenic cyst, Congenital pulmonary airway malformations, Dysontogenic tumor, PPB registry, Primitive neuroectodermal tumors

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How to Cite this Article

Pubmed Style

Sarangi PK, Sagar HS, Nahak SK, Mohanty J, Parida S. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. 2017; 7(1): 67-71. doi:10.5455/jmas.252500

Web Style

Sarangi PK, Sagar HS, Nahak SK, Mohanty J, Parida S. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. https://jmas.in/?mno=252500 [Access: June 27, 2026]. doi:10.5455/jmas.252500

AMA (American Medical Association) Style

Sarangi PK, Sagar HS, Nahak SK, Mohanty J, Parida S. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. 2017; 7(1): 67-71. doi:10.5455/jmas.252500

Vancouver/ICMJE Style

Sarangi PK, Sagar HS, Nahak SK, Mohanty J, Parida S. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. (2017), [cited June 27, 2026]; 7(1): 67-71. doi:10.5455/jmas.252500

Harvard Style

Sarangi, P. K., Sagar, . H. S., Nahak, . S. K., Mohanty, . J. & Parida, . S. (2017) Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci, 7 (1), 67-71. doi:10.5455/jmas.252500

Turabian Style

Sarangi, Pradosh Kumar, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, and Sasmita Parida. 2017. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. Journal of Medical and Allied Sciences, 7 (1), 67-71. doi:10.5455/jmas.252500

Chicago Style

Sarangi, Pradosh Kumar, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, and Sasmita Parida. "Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature." Journal of Medical and Allied Sciences 7 (2017), 67-71. doi:10.5455/jmas.252500

MLA (The Modern Language Association) Style

APA (American Psychological Association) Style

Sarangi, P. K., Sagar, . H. S., Nahak, . S. K., Mohanty, . J. & Parida, . S. (2017) Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. Journal of Medical and Allied Sciences, 7 (1), 67-71. doi:10.5455/jmas.252500


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